Journal of Indian Academy of Oral Medicine and Radiology

CASE REPORT
Year
: 2008  |  Volume : 20  |  Issue : 1  |  Page : 36--40

Papillon Lefèvre syndrome: A report of 3 cases with review of literature


Anita Munde, Manjiri Joshi, Sonia Sagoo, Safia Shoeb 
 Department of Oral Medicine and Radiology, Rural Dental College of Pravara Institute of Medical Sciences, Loni-413 736, Rahata, Ahmednagar, Maharashtra, India

Correspondence Address:
Anita Munde
Department of Oral Medicine and Radiology, Rural Dental College of Pravara Institute of Medical Sciences, Loni 413736, Tal- Rahata, Dist- Ahmednagar, Maharashtra
India

Papillon Lefèvre syndrome (PLS) is a rare autosomal recessive disorder of keratinisation characterized by palmoplantar hyperkeratosis, periodontopathy and precocious (premature) loss of dentition. Exact mechanism of these clinical events mainly remains speculative. The periodontitis in PLS is usually difficult to control. Effective treatment includes extraction of primary teeth combined with oral antibiotics and professional teeth cleaning. Dentists play a significant role in the diagnosis and management of PLS patients. This paper describes 3 cases of PLS reporting to the out patient department within a span of 2 years with classic clinical features and briefly reviews the literature.


How to cite this article:
Munde A, Joshi M, Sagoo S, Shoeb S. Papillon Lefèvre syndrome: A report of 3 cases with review of literature.J Indian Acad Oral Med Radiol 2008;20:36-40


How to cite this URL:
Munde A, Joshi M, Sagoo S, Shoeb S. Papillon Lefèvre syndrome: A report of 3 cases with review of literature. J Indian Acad Oral Med Radiol [serial online] 2008 [cited 2022 Aug 14 ];20:36-40
Available from: https://www.jiaomr.in/article.asp?issn=0972-1363;year=2008;volume=20;issue=1;spage=36;epage=40;aulast=Munde;type=0