Journal of Indian Academy of Oral Medicine and Radiology

SHORT COMMUNICATION
Year
: 2007  |  Volume : 19  |  Issue : 4  |  Page : 575--584

Complete Tri Symptomatic Sturge Weber Syndrome - A case report with review of literature


Karthik Hegde1, R Gopakumar2, Subhas Babu1, S Giridhar Naidu1, Vidya Ajila1, R Kamala1 
1 Dept. Of Oral Medicine & Radiology, A.B. Shetty Memorial Institute of Dental Sciences, Deralakatte, Mangalore, India
2 Dept. Of Oral Medicine & Radiology, Mahatma Gandhi Dental College & Hospital, Jaipur, India

Correspondence Address:
Karthik Hegde
Dept. Of Oral Medicine & Radiology, A.B. Shetty Memorial Institute of Dental Sciences, Deralakatte, Mangalore
India

Sturge-Weber syndrome (SWS) belongs to a group of disorders collectively known as the phakomatoses («DQ»mother-spot«DQ» diseases). It consists of congenital hamartomatous malformations that may affect the eye, skin, and central nervous system at different times. Sturge-Weber syndrome is rare. It is present at birth in about 1 in every 50,000 babies. SWS is classified into complete trisymptomatic SWS when all 3 organ systems are involved, incomplete bisymptomatic SWS when the involvement is either oculocutaneous or neurocutaneous, and incomplete monosymptomatic SWS when there is only neural or cutaneous involvement. Patients with no cutaneous involvement appear to be spared from the ocular manifestations of the syndrome. Presenting a case report of this rare disorder in a 26 year old male, who presented with lip enlargement.


How to cite this article:
Hegde K, Gopakumar R, Babu S, Naidu S G, Ajila V, Kamala R. Complete Tri Symptomatic Sturge Weber Syndrome - A case report with review of literature.J Indian Acad Oral Med Radiol 2007;19:575-584


How to cite this URL:
Hegde K, Gopakumar R, Babu S, Naidu S G, Ajila V, Kamala R. Complete Tri Symptomatic Sturge Weber Syndrome - A case report with review of literature. J Indian Acad Oral Med Radiol [serial online] 2007 [cited 2022 Aug 9 ];19:575-584
Available from: https://www.jiaomr.in/article.asp?issn=0972-1363;year=2007;volume=19;issue=4;spage=575;epage=584;aulast=Hegde;type=0